A case of congenital hemihypertrophy, which affects the right part hemi-tongue and the homolateral superior member, is reported in a just born of feminine sex, this patient has been observed until the age of one year and five months, at this age she was not controlled any more. Then the clinic history is reviewed and the clinic, associate congenital defects, are commented, also the existence of embryonal tumours, possible etiopathogenic hypothesis, treatment and prognostic.