OBJECTIVE: Sarcomas arising from the urinary tract are rare, representing less than 2% of all urologic tumors. The paratesticular region is one of the most unfrequent locations. Leiomyosarcoma, rhabdomyo-sarcoma, liposarcoma, malignant fibrohistiocytoma, etc. and the combination of two or more histological types has exceptionally been reported . We describe the case of a patient with a mixed paratesticular sarcoma and perform a bi-bliographic review. METHODS: The patient underwent right radical orchyectomy and the surgical specimen was sent to pathologic study. RESULTS: There are no previous case reports in the literature of paratesticular mixed tumor with liposarcoma and rhabdomyosarcoma. CONCLUSIONS: Sarcomas of the spermatic cord are rare neoplasias and should be considered on the differencial diagnosis of scrotal masses. The treatment of choice is surgical and adjuvant treatment must be individualized depending on tumor aggressiveness.